Chawes Bo L K, Jensen Tim, Olsen Rúna, Joensen Frói, Nielsen Kim G, Buchvald Frederik
BørneUngeKlinikken, Dansk BørneLungeCenter, Juliane Marie Centret, Rigshospitalet, Blegdamsvej 9, 2100 København Ø, Denmark.
Ugeskr Laeger. 2012 Jun 11;174(24):1674-5.
Plastic bronchitis is a rare complication in children with inflammatory lung disease and postoperatively after Fontan operation for congenital heart disease. Plastic bronchitis is characterised by expectoration of large bronchial casts, which can cause fatal airway obstruction. We describe a case of a ten year-old boy with transposition vasorum and hypoplastic right ventricle who underwent a Fontan operation at the age of three. Seven years postoperatively he developed plastic bronchitis which was treated with mucolytics, inhaled corticosteroids, β2-agonist, hypertonic NaCl, and chest physiotherapy, resulting in partial recovery.
塑性支气管炎是患有炎性肺病的儿童以及先天性心脏病行Fontan手术后的一种罕见并发症。塑性支气管炎的特征是咳出大的支气管铸型,可导致致命的气道阻塞。我们描述了一例10岁男孩,患有血管移位和右心室发育不全,3岁时接受了Fontan手术。术后7年,他患上了塑性支气管炎,接受了黏液溶解剂、吸入性糖皮质激素、β2受体激动剂、高渗氯化钠和胸部物理治疗,部分康复。