Karlsen Stine, Nielsen Dennis Tønner, Grønbæk Henning
Medicinsk Afdeling V, Hepatologi og Gastroenterologi, Aarhus Universitetshospital, Nørrebrogade 44, 8000 Aarhus C, Denmark.
Ugeskr Laeger. 2012 Jun 11;174(24):1677-9.
Budd-Chiari syndrome (BCS) is a rare disease defined by congestive hepatopathy with obstruction of the hepatic venous outflow tract. Classical symptoms and signs include ascites, hepatomegaly, abdominal pain and various degrees of liver dysfunction. BCS is predominantly caused by thrombosis, malformations and venous compression. We present a case, in which BCS was the cause of liver cirrhosis complicated with refractory ascites and which can be misinterpreted as hepatocellular carcinoma nodules. The diagnosis was confirmed during the transjugular intrahepatic portosystemic shunt procedure with successful vascular stenting resolving the ascites formation.
布加综合征(BCS)是一种罕见疾病,其定义为伴有肝静脉流出道梗阻的充血性肝病。典型症状和体征包括腹水、肝肿大、腹痛以及不同程度的肝功能障碍。BCS主要由血栓形成、畸形和静脉受压引起。我们报告一例病例,其中布加综合征是肝硬化合并难治性腹水的病因,且可能被误诊为肝细胞癌结节。在经颈静脉肝内门体分流术过程中确诊,成功进行血管支架置入术解决了腹水形成问题。