Bhardwaj Anand Kumar, Sharma Prem Dass, Mittal Amit, Sharma Akshay
Paediatrics Department, MM Institute of Medical Sciences and Research, Ambala, Haryana, India.
BMJ Case Rep. 2011 Aug 17;2011:bcr0520114171. doi: 10.1136/bcr.05.2011.4171.
Cystic nephroma is a rare benign renal neoplasm that is purely cystic and is lined by an epithelium. Bilateral cystic nephromas are even rarer with only a handful cases reported in the literature. A case of a 2-year-old male child who presented with bilateral renal cystic masses later diagnosed as cystic nephromas is presented here. Ultrasound, CT scan and histopathological investigations aided in arriving at the correct diagnosis. The most concerning feature was the presence of a fluid filled cystic mass in the lungs, most probably a pleuropulmonary blastoma which is a rare malignant neoplasm known to be associated with bilateral cystic nephromas. The most common presenting symptoms of cystic nephroma are painless abdominal mass, abdominal or flank pain and haematuria. These tumours usually follow a benign course and nephrectomy alone is curative. A close surveillance of such patients is recommended because of elevated risk of other tumours.
囊性肾瘤是一种罕见的良性肾肿瘤，完全为囊性且内衬上皮。双侧囊性肾瘤更为罕见，文献中仅报道了少数病例。本文介绍了一例2岁男童，其双侧肾出现囊性肿块，后来被诊断为囊性肾瘤。超声、CT扫描和组织病理学检查有助于做出正确诊断。最令人担忧的特征是肺部存在一个充满液体的囊性肿块，很可能是胸膜肺母细胞瘤，这是一种罕见的恶性肿瘤，已知与双侧囊性肾瘤有关。囊性肾瘤最常见的症状是无痛性腹部肿块、腹部或侧腹痛以及血尿。这些肿瘤通常呈良性病程，单纯肾切除术即可治愈。由于其他肿瘤的风险升高，建议对这类患者进行密切监测。
