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一名暴发性心肌炎患儿的非典型起病及病程

Atypical onset and course in a child with fulminant myocarditis.

作者信息

Rocchi A, Mazzoni M, Bertolozzi G, Milani G, Napolitano L, Colli A, Rizzuti T, Bianchetti M, Plebani A, Laicini E, Fossali E

机构信息

Cà Granda Maggiore Hospital , IRCCS Foundation, Milan, Italy.

出版信息

Minerva Pediatr. 2012 Aug;64(4):447-50.

PMID:22728616
Abstract

We report a fatal case of fulminant myocarditis (FM) in a five-year-old male child. He presented to our Emergency Department having complained fever, vomiting, nausea and abdominal pain from the previous day. The ECG showed broad complex tachycardia unresponsive to treatment with both drugs and all other resuscitation measures and the child died four hours after admission. Post-mortem histological examination showed diffuse infiltration of the myocardium although no viral material could be identified. FM is relatively uncommon and late presentation at an almost irreversible stage unusual. This case indicates the necessity of a rapid transfer to a center with ECMO or MCS, when FM is diagnosed.

摘要

我们报告了一例5岁男童暴发性心肌炎(FM)致死病例。他因前一日出现发热、呕吐、恶心和腹痛前来我院急诊科就诊。心电图显示宽QRS波心动过速,药物治疗及所有其他复苏措施均无效,患儿入院4小时后死亡。尸检组织学检查显示心肌弥漫性浸润,但未发现病毒物质。FM相对少见,在几乎不可逆阶段的晚期表现也不常见。该病例表明,诊断为FM时,有必要迅速转至具备体外膜肺氧合(ECMO)或机械循环支持(MCS)的中心。

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