Kelley Brian C, Arnold Paul M, Grant John A, Newell Kathy L
Department of Neurosurgery, University of Kansas Medical Center, 3901 Rainbow Boulevard, Kansas City, Kansas 66160, USA.
J Neurosurg Pediatr. 2012 Aug;10(2):121-5. doi: 10.3171/2012.4.PEDS1216. Epub 2012 Jun 29.
The authors present a rare case of primary intracranial leiomyosarcoma (LMS) in a young, immunocompetent boy. The patient presented with an expanding right forehead mass. Diagnostic workup revealed multiple large intracranial tumors. The largest mass was resected, and pathological analysis revealed LMS. Given the poor prognosis of this tumor, the family declined further care, and the child died 3 months later. Primary LMSs are extremely rare tumors in the pediatric population, especially in patients who are not immunocompromised.
作者报告了一例发生在一名免疫功能正常的年轻男孩身上的原发性颅内平滑肌肉瘤（LMS）罕见病例。该患者表现为右侧前额肿物进行性增大。诊断性检查发现颅内有多个大肿瘤。切除了最大的肿物，病理分析显示为LMS。鉴于该肿瘤预后较差，家属拒绝进一步治疗，患儿3个月后死亡。原发性LMS在儿科人群中极为罕见，尤其是在非免疫功能低下的患者中。
