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肉芽肿性多血管炎最初被误诊为肺癌。

Granulomatosis with polyangiitis initially misdiagnosed as lung cancer.

作者信息

Campainha S, Gonçalves M, Tavares V, Castelões P, Marinho A, Neves S

机构信息

Serviço de Pneumologia, Centro Hospitalar de Vila Nova de Gaia/Espinho EPE, Vila Nova de Gaia, Portugal.

出版信息

Rev Port Pneumol. 2013 Jan-Feb;19(1):45-8. doi: 10.1016/j.rppneu.2012.04.002. Epub 2012 Jun 29.

DOI:10.1016/j.rppneu.2012.04.002
PMID:22748944
Abstract

Granulomatosis with Polyangiitis (GPA), which was formerly named Wegener's Granulomatosis (WG) is a systemic disease characterized by necrotizing granulomatous inflammation and vasculitis that primarily involves upper and lower respiratory tract, as well as kidneys. Diagnosing GPA on the basis of transthoracic fine needle aspiration (TFNA) may be problematic, as it can be misdiagnosed as cancer. We describe a patient with a probable GPA which was originally diagnosed as malignancy, but who responded to lung cancer chemotherapy.

摘要

肉芽肿性多血管炎(GPA),以前称为韦格纳肉芽肿(WG),是一种全身性疾病,其特征为坏死性肉芽肿性炎症和血管炎,主要累及上、下呼吸道以及肾脏。基于经胸细针穿刺抽吸(TFNA)诊断GPA可能存在问题,因为它可能被误诊为癌症。我们描述了一名可能患有GPA的患者,该患者最初被诊断为恶性肿瘤,但对肺癌化疗有反应。

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