Lee Seung Hyun, Kim Jae Bum, Park Nam Hee, Kim Hyung Seop, Keum Dong Yoon
Department of Thoracic and Cardiovascular Surgery, Dongsan Medical Center, University of Keimyung College of Medicine, Daegu, Republic of Korea.
Thorac Cardiovasc Surg. 2013 Jun;61(4):327-9. doi: 10.1055/s-0032-1311546. Epub 2012 Jul 12.
We report the case of an adult patient with the unusual combination of a perimembranous (PM) ventricular septal defect (VSD), asymptomatic ruptured sinus of Valsalva communicating with the right ventricle, and a bicuspid aortic valve. Bulged sinus of Valsalva might conceal the small PM VSD, therefore the patient had no symptom-associated VSD until grown up. However, when aortic valve regurgitation associated with prolapsed right aortic cusp worsened and ruptured sinus of Valsalva was found by echocardiogram, the patient underwent aortic valve replacement with anatomical surgical correction of the aortic sinus and VSD.
我们报告了一例成年患者，其患有膜周部（PM）室间隔缺损（VSD）、与右心室相通的无症状性瓦氏窦破裂以及二叶式主动脉瓣这一不寻常的组合。膨出的瓦氏窦可能掩盖了小的膜周部室间隔缺损，因此该患者在成年前一直没有与室间隔缺损相关的症状。然而，当与右主动脉瓣叶脱垂相关的主动脉瓣反流加重且经超声心动图发现瓦氏窦破裂时，该患者接受了主动脉瓣置换术，并对主动脉窦和室间隔缺损进行了解剖学手术矫正。
