Rigault P, Padovani J P
Service d'Orthopédie Traumatologie infantile de l'hôpital des Enfants-Malades, Paris.
Chirurgie. 1990;116(3):312-4.
This paper is the report of three cases of spinal deformities connected to a paravertebral ganglioneuroma: The first case was discovered during the anterior approach of a thoracic scoliosis of more than 100 degrees at the age of twelve; the child had been treated before the age of one year for a thoracic neuroblastoma; eleven years after removal of the ganglioneuroma and fusion of the spinal curve, the evolution is satisfactory. The second case was similar, but the initial findings during infancy were not well known; the result is good two years after excision of the tumor and fusion of the spine. The third case is simply a progressive kyphosis after removal of a thoracic ganglioneuroma by laminectomy at the age of five years. The sister of this child suffered of a malignant thoracic neuroblastoma. Are pointed out here below the nature of these ganglioneuromas, non-secreting tumors from neuroectodermic origin, their rarity in relation with spinal deformities, the difficulties of their detection by modern imaging, and the requirement of a close survey of these patients and their family.
本文报告了3例与椎旁神经节神经瘤相关的脊柱畸形病例：第一例在12岁时行前路手术治疗超过100度的胸椎侧弯时被发现；该患儿在1岁前曾接受过胸段神经母细胞瘤治疗；神经节神经瘤切除及脊柱融合术后11年，病情进展令人满意。第二例情况相似，但婴儿期的最初表现不详；肿瘤切除及脊柱融合术后两年效果良好。第三例是一名5岁患儿在接受椎板切除术后切除胸段神经节神经瘤后出现的进行性后凸畸形。该患儿的姐姐患有恶性胸段神经母细胞瘤。以下指出了这些神经节神经瘤的性质，即神经外胚层起源的无分泌功能肿瘤，它们与脊柱畸形相关的罕见性，现代影像学检测它们的困难，以及对这些患者及其家族进行密切随访的必要性。
