Al-Hammadi Suleiman, Al-Reyami Eiman, Al-Remeithi Sareea, Al-Zaabi Khawla, Al-Zir Rola, Al-Sagban Heba, Zoubaidi Taoufik, Souid Abdul-Kader
Department of Pediatrics, UAE University, Al-Ain, United Arab Emirates.
BMC Res Notes. 2012 Jul 31;5:393. doi: 10.1186/1756-0500-5-393.
Primary immunodeficiency (PID) is a cluster of serious disorders that requires special alertness on the part of the medical staff for prompt diagnosis and management of the patient. This study explored PID knowledge and experience among pediatricians of wide educational backgrounds, practicing in the United Arab Emirates (UAE).
A self-administered questionnaire was used to determine the competency of pediatricians in their knowledge of PID disorders. This study questionnaire included questions on PID signs and symptoms, syndromes associated with immunodeficiency, screening tests, interpreting laboratory tests and case management. The participants were 263 pediatricians of diverse education working in the 27 governmental hospitals in all regions of UAE.
The overall performance of the pediatricians did not differ based on their age, gender, origin of certification, rank, or years of experience. Of the 50 questions, 20% of pediatricians answered correctly <60% of the questions, 76% answered correctly 60 to 79% of the questions, and 4% answered correctly ≥80% of the questions. Seventeen of the 19 PID signs and symptoms were identified by 55 to 97%. Four of 5 syndromes associated with immunodeficiency were identified by 50 to 90%. Appropriate screening tests were chosen by 64 to 96%. Attention to the laboratory reference range values as function of patient age was notably limited.
There was a noteworthy deficiency in PID work-up. Therefore, implementing effective educational strategies is needed to improve the competency of pediatricians to diagnose and manage PID disorders.
原发性免疫缺陷病（PID）是一组严重疾病，需要医护人员保持特别警惕，以便对患者进行及时诊断和管理。本研究探讨了在阿拉伯联合酋长国（阿联酋）执业的、具有广泛教育背景的儿科医生对PID的了解情况和经验。
采用自填式问卷来确定儿科医生对PID疾病的知识掌握程度。本研究问卷包括关于PID体征和症状、与免疫缺陷相关的综合征、筛查测试、解读实验室检查结果及病例管理等问题。参与者为在阿联酋所有地区的27家政府医院工作的263名不同学历的儿科医生。
儿科医生的总体表现不因年龄、性别、认证来源、职级或工作经验而有所不同。在50道题中，20%的儿科医生正确回答的问题不到60%，76%的儿科医生正确回答了60%至79%的问题，4%的儿科医生正确回答了≥80%的问题。19种PID体征和症状中有17种被55%至97%的人识别出来。5种与免疫缺陷相关的综合征中有4种被50%至90%的人识别出来。64%至96%的人选择了合适的筛查测试。对实验室参考范围值随患者年龄变化的关注明显有限。
在PID检查方面存在明显不足。因此，需要实施有效的教育策略来提高儿科医生诊断和管理PID疾病的能力。
