Quartuccio Luca, Tuniz Francesco, Petralia Benedetto, Zanotti Bruno, Skrap Miran, Vita Salvatore De
Clinic of Rheumatology, Azienda Ospedaliero-Universitaria di Udine, DSMB, Italy.
Open Rheumatol J. 2012;6:175-9. doi: 10.2174/1874312901206010175. Epub 2012 Jul 25.
Benign angiopathy of the central nervous system is a clinical syndrome with evidence of reversible cerebral vasoconstriction (RCVS). Haemorrhagic stroke, either subarachnoid or intracerebral is an unusual presentation of RCVS. We describe a case of RCVS presenting with a subarachnoid haemorrhage (SAH), with rebleeding and onset of hydrocephalus during the first week, and, notably, delayed evidence of typical angiographic features after two negative prior exams. Normalization of the angiographic vasculitic-like lesions was documented at month +6. Repeated cerebral angiograms are mandatory to exclude this kind of disease, and the uncommon presentation of this case reinforces this concept.
中枢神经系统良性血管病是一种具有可逆性脑血管收缩（RCVS）证据的临床综合征。蛛网膜下腔出血或脑内出血性卒中是RCVS的一种不常见表现。我们描述了一例以蛛网膜下腔出血（SAH）为表现的RCVS病例，该病例在第一周内出现再出血和脑积水，值得注意的是，在之前两次检查结果为阴性后，典型血管造影特征出现延迟。在第6个月记录到血管造影显示的血管炎样病变恢复正常。必须重复进行脑血管造影以排除此类疾病，该病例的罕见表现强化了这一观念。
