Yuan Ting, Luo Bai-Ling, Gu Qi-Hua, Yao Ji
Department of Respiratory Medicine, Xiang Ya Hospital, Central South University, Changsha, Hunan province 410008, China.
Multidiscip Respir Med. 2012 Jul 18;7(1):17. doi: 10.1186/2049-6958-7-17.
Neurogenic tumor of lung is very rare. Only few cases have been reported in the literature. We present here two cases of bronchopulmonary neurofibromatosis in two adults. In both cases, attempts at imaging failed to diagnose the case, and it was the histological study that ensured the diagnosis of neurofibromatosis. Biopsy specimens showed bundles of spindle-shaped cells mixed with collagen, and on immunohistochemistry some cells were positive for S-100 protein.
肺神经源性肿瘤非常罕见。文献中仅报道过少数病例。我们在此呈现两例成人支气管肺神经纤维瘤病病例。在这两例病例中，影像学检查均未能确诊，最终是组织学研究确诊了神经纤维瘤病。活检标本显示有成束的梭形细胞与胶原混合，免疫组织化学检测显示部分细胞S-100蛋白呈阳性。
