Zhang Jiexiu, Song Ninghong, Liu Bianjiang, Hua Lixin, Wang Zengjun, Yin Changjun, Zhang Wei
Department of Urology, The First Affiliated Hospital of Nanjing Medical University, Nanjing, China.
Urol Int. 2012;89(3):369-72. doi: 10.1159/000341691. Epub 2012 Sep 4.
Castleman's disease (CD) is an uncommon disorder of the lymphoid hyperplasia. It is especially rare in the retroperitoneum or perirenal area. We report the case of a 62-year-old woman who had an abdominal mass localized above the right kidney in the region of the right adrenal gland found by computed tomography scan. The patient subsequently underwent an exploratory laparotomy. Pathological examination revealed retroperitoneal localized CD (LCD) of the hyaline vascular type. Diversity of disease sites and nonspecificity of clinical manifestations lead to diagnostic difficulties. Therefore, diagnosis is mainly achieved via lymph node biopsy or pathological examination. Like in the reported case, LCD usually has a good prognosis after complete resection of the lesion.
卡斯特曼病(CD)是一种罕见的淋巴组织增生性疾病。它在腹膜后或肾周区域尤为罕见。我们报告一例62岁女性病例,通过计算机断层扫描发现其右肾上腺区域右肾上方有一腹部肿块。患者随后接受了剖腹探查术。病理检查显示为透明血管型腹膜后局限性卡斯特曼病(LCD)。疾病部位的多样性和临床表现的非特异性导致诊断困难。因此,诊断主要通过淋巴结活检或病理检查来实现。如本报告病例所示,LCD在病变完全切除后通常预后良好。