Department of Diagnostic and Interventional Radiology, University of Tuebingen, Hoppe-Seyler-Str. 3, 72076 Tuebingen, Germany.
J Pediatr Surg. 2012 Sep;47(9):E23-8. doi: 10.1016/j.jpedsurg.2012.04.011.
Extrahepatic portal vein (PV) obstruction (EHPVO) is a rare disorder in early childhood with unknown incidence and mostly unknown etiology. In children with EHPVO, the hepatopedal flow of the mesenteric venous blood is hindered by an obstruction of the PV resulting in prehepatic portal hypertension. The curative treatment with a meso-Rex shunt connects the superior mesenteric vein to the left PV by a venous autograft. Despite good primary patency, reocclusion of a meso-Rex bypass and its treatment can be challenging. We present 2 patients with EHPVO with subtotal functional occlusion of a meso-Rex shunt treated by percutaneous interventions with short- and mid-term follow-up.
肝外门静脉(PV)阻塞(EHPVO)在儿童早期是一种罕见疾病,其发病率未知,病因大多未知。在患有 EHPVO 的儿童中,肠系膜静脉血液的肝向血流被 PV 阻塞所阻碍,导致肝前门静脉高压。通过静脉自体移植将肠系膜上静脉与左 PV 连接起来的间置-Rex 分流术是一种根治性治疗方法。尽管初次通畅性良好,但间置-Rex 旁路的再闭塞及其治疗可能具有挑战性。我们介绍了 2 例 EHPVO 患者,他们的间置-Rex 分流术存在部分功能性闭塞,通过经皮介入治疗,取得了短期和中期随访结果。