Universidad Central del Caribe, School of Medicine, Bayamón, PR 00912.
J Pediatr Surg. 2012 Sep;47(9):E29-32. doi: 10.1016/j.jpedsurg.2012.04.017.
Ganglioneuromas are benign tumors originating from the neural crest and are composed of mature ganglion cells. We describe a 15-year-old normotensive adolescent girl with a 2-month history of left flank pain. Imaging revealed a left suprarenal mass with elevated urinary dopamine level. During laparoscopic adrenalectomy, intraoperative rebound hypertension occurred. After resection, dopamine levels normalized. The pathologic diagnosis revealed an adrenal ganglioneuroma.
神经节细胞瘤起源于神经嵴,是良性肿瘤,由成熟的神经节细胞组成。我们描述了一例 15 岁的血压正常青少年女性,有 2 个月的左侧腰部疼痛史。影像学检查显示左肾上腺有肿块,尿多巴胺水平升高。在腹腔镜肾上腺切除术期间,出现术中血压反跳性升高。切除后,多巴胺水平恢复正常。病理诊断为肾上腺神经节细胞瘤。