Department of Pediatrics, Peking University First Hospital, Beijing, China.
Korean Circ J. 2012 Aug;42(8):513-8. doi: 10.4070/kcj.2012.42.8.513. Epub 2012 Aug 31.
Pulmonary hypertension (PH) is a clinical hemodynamic syndrome characterized by increased pulmonary artery pressure and pulmonary vascular resistance. It can cause right ventricular failure, and even death. Pediatric PH is not very common, but is a greatly hazardous disease that leads to a high mortality rate. Therefore, many registry organizations have been established in the world to strengthen the study of diagnosis and treatment of the disease, and improve the understanding of pediatric PH. This article reviewed recently published researches, as well as presented a comprehensive understanding of PH, including definition, classification, epidemiology, prognosis and treatment.
肺动脉高压(PH)是一种以肺动脉压和肺血管阻力升高为特征的临床血流动力学综合征。它可导致右心衰竭,甚至死亡。儿科 PH 并不常见,但却是一种危害极大的疾病,导致死亡率很高。因此,世界上许多登记组织已经成立,以加强对该病的诊断和治疗的研究,并提高对儿科 PH 的认识。本文综述了最近发表的研究,并对 PH 的定义、分类、流行病学、预后和治疗进行了全面的了解。