Department of Cardiovascular Surgery, Istanbul University, Istanbul Medical Faculty, Turkey.
Eur J Vasc Endovasc Surg. 2012 Nov;44(5):482-4. doi: 10.1016/j.ejvs.2012.08.004. Epub 2012 Sep 14.
The Ehlers-Danlos Syndrome (EDS) is a rare connective tissue disorder characterised by fragility of the soft connective tissues and widespread manifestations in skin, ligaments, joints, blood vessels and internal organs. We report a case of a 12-year-old boy, previously diagnosed with kyphoscoliosis-type EDS (type VI), presenting with a left brachial artery pseudo-aneursym with history of multiple spontaneous and post-traumatic arterial ruptures. Surgical management of this patient was performed successfully by primary repair of brachial artery lesion.
埃勒斯-当洛斯综合征（EDS）是一种罕见的结缔组织疾病，其特征是软结缔组织脆弱，皮肤、韧带、关节、血管和内脏广泛受累。我们报告了一例 12 岁男孩的病例，该患者先前被诊断为脊柱后侧凸型 EDS（六型），有多次自发性和外伤性动脉破裂史，现出现左侧肱动脉假性动脉瘤。该患者的手术治疗通过肱动脉病变的一期修复成功完成。
