Shringarpure Sanish S, Thachil Joseph V, Maya Menon
Department of Urology, Apollo Hospitals, Chennai, Tamil Nadu, India.
Saudi J Kidney Dis Transpl. 2012 Sep;23(5):1032-4. doi: 10.4103/1319-2442.100943.
Perivascular epithelioid cell tumors are a family of related mesenchymal neoplasms that include angiomyolipoma, lymphangiomyomatosis, clear cell sugar tumor of the lung and a group of rare morphologically and immunophenotypically similar lesions that show immunoreactivity for both melanocytic (HMB-45 and/or melan-A) and smooth muscle (actin and/or desmin) markers. This case is presented for its rare occurrence and characteristic morphologic and immunohistochemical features.
血管周上皮样细胞瘤是一组相关的间质性肿瘤，包括血管平滑肌脂肪瘤、淋巴管平滑肌瘤病、肺透明细胞瘤以及一组罕见的形态学和免疫表型相似的病变，这些病变对黑素细胞（HMB-45和/或黑素A）和平滑肌（肌动蛋白和/或结蛋白）标志物均呈免疫反应性。本文报告此病例是因其罕见的发生率以及特征性的形态学和免疫组化特征。
