Behrndtz Anne, Andersen Grethe, Simonsen Claus Z
Neurologisk Afdeling, Aarhus Universitetshospital, Aarhus, Denmark.
Ugeskr Laeger. 2012 Sep 17;174(38):2237-8.
Superficial siderosis (SS) of the central nervous system is a rare disorder in which the most common clinical manifestations are gait ataxia, sensorineural deafness and affection of the corticospinal tracts. Knowledge of this disorder is important since early diagnosis and treatment is crucial for the prognosis. Furthermore, new treatment strategies are emerging. The effect of corticosteroids on SS without an identifiable bleeding source has been debated. We present a case with a good clinical effect of steroids.
中枢神经系统表面铁沉积症(SS)是一种罕见的疾病,其最常见的临床表现为步态共济失调、感音神经性耳聋和皮质脊髓束受累。了解这种疾病很重要,因为早期诊断和治疗对预后至关重要。此外,新的治疗策略正在出现。皮质类固醇对无明确出血源的SS的疗效一直存在争议。我们报告一例使用类固醇后临床效果良好的病例。