Kansal Ritesh, Mahore Amit, Dange Nitin, Kukreja Sanjay
Seth G.S. Medical College at K.E.M. Hospital, Department of Neurosurgery, Parel, Mumbai, Indian.
Turk Neurosurg. 2012;22(5):659-61. doi: 10.5137/1019-5149.JTN.3985-10.1.
The Currarino triad, also known as the "Currarino Syndrome", is a rare complex of congenital caudal anomalies including three main features; a sacral bony deformity, anorectal malformations, and a presacral mass. We present an extremely uncommon case of Currarino syndrome in adulthood presenting with repeated episodes of meningitis. Magnetic resonance imaging of spine was suggestive of caudal regression. Cord was low lying, conus ending at L3 level with evidence of tethering at that level. A large cyst was noted in the sacral canal extending forwards in the pelvis through the widened sacral foramina on right side. She was operated through a posterior approach, via sacral laminectomy. Dura was opened in the midline, large silvery white epidermoid tumor was found completely occupying the anterior sacral meningocele. The case and relevant literature is discussed.
库拉里诺三联征,也称为“库拉里诺综合征”,是一种罕见的先天性尾部异常复合体,包括三个主要特征:骶骨骨质畸形、肛门直肠畸形和骶前肿块。我们报告一例极其罕见的成年期库拉里诺综合征病例,该患者反复发生脑膜炎。脊柱磁共振成像提示尾部退化。脊髓低位,圆锥终止于L3水平,该水平有脊髓栓系证据。在骶管内发现一个大囊肿,通过右侧增宽的骶孔向前延伸至盆腔。她通过后路手术,即骶椎板切除术进行治疗。硬脑膜在中线打开,发现一个大的银白色表皮样肿瘤完全占据了骶前脊膜膨出。本文对该病例及相关文献进行了讨论。