• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利:CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验

早期诊断脱髓鞘疾病的视觉诱发电位——一例 Devic 病报告。

Visual evoked potentials in early diagnosis of demyelinating diseases--a case report of Devic's disease.

机构信息

Department of Ophthalmology, Warsaw Medical University, Warsaw, Poland.

出版信息

Med Sci Monit. 2012 Oct;18(10):CS82-4. doi: 10.12659/msm.883473.

DOI:10.12659/msm.883473
PMID:23018359
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3560553/
Abstract

BACKGROUND

Devic's disease, also known as neuromyelinitis optica (NMO), is a severe, rare demyelinating disorder, previously considered to be a form of multiple sclerosis (MS). The aim of this study was to present the case report of 21-year-old woman with a very early diagnosis of Devic's disease, established following electrophysiological testing.

CASE REPORT

A 21-year-old woman was referred to Warsaw Medical University, Department of Ophthalmology, with subjective visual impairment. The patient underwent a full clinical examination, colour vision and Goldmann visual field testing, fluorescein angiography, OCT, multifocal ERG, and visual evoked potentials (VEPs).

CONCLUSIONS

Visual evoked potentials are a very useful diagnostic tool in optic nerve neuropathies. In our patient, the electrophysiological testing allowed us to establish a proper diagnosis very early, before typical clinical signs of Devic's disease.

摘要

背景

Devic 病,又称视神经脊髓炎(NMO),是一种严重的、罕见的脱髓鞘疾病,以前被认为是多发性硬化症(MS)的一种形式。本研究的目的是报告一例 21 岁女性的病例,该患者在电生理测试后被极早期诊断为 Devic 病。

病例报告

一名 21 岁女性因主观视力障碍被转诊至华沙医科大学眼科系。该患者接受了全面的临床检查、色觉和 Goldmann 视野检查、荧光素血管造影、OCT、多焦 ERG 和视觉诱发电位(VEP)。

结论

视觉诱发电位是视神经病变非常有用的诊断工具。在我们的患者中,电生理测试使我们能够在 Devic 病的典型临床症状出现之前,非常早期地做出明确诊断。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35dd/3560553/9e38d492200d/medscimonit-18-10-CS82-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35dd/3560553/9e38d492200d/medscimonit-18-10-CS82-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/35dd/3560553/9e38d492200d/medscimonit-18-10-CS82-g001.jpg

相似文献

1
Visual evoked potentials in early diagnosis of demyelinating diseases--a case report of Devic's disease.早期诊断脱髓鞘疾病的视觉诱发电位——一例 Devic 病报告。
Med Sci Monit. 2012 Oct;18(10):CS82-4. doi: 10.12659/msm.883473.
2
Devic's disease before Devic: Bilateral optic neuritis and simultaneous myelitis in a young woman (1874).德维克病出现之前的德维克病:一名年轻女性(1874年)的双侧视神经炎和同时性脊髓炎
J Neurol Sci. 2015 Nov 15;358(1-2):419-21. doi: 10.1016/j.jns.2015.08.022. Epub 2015 Aug 15.
3
Devic's neuromyelitis optica in an infant case.婴儿期的视神经脊髓炎谱系疾病病例
J Child Neurol. 2007 Sep;22(9):1143-6. doi: 10.1177/0883073807306270.
4
Devic's index case: A critical reappraisal - AQP4-IgG-mediated neuromyelitis optica spectrum disorder, or rather MOG encephalomyelitis?德维克病例:批判性再评价——AQP4-IgG 介导的视神经脊髓炎谱系疾病,还是 MOG 脑炎?
J Neurol Sci. 2019 Dec 15;407:116396. doi: 10.1016/j.jns.2019.07.014. Epub 2019 Jul 11.
5
Devic's neuromyelitis optica: clinical and imaging findings.视神经脊髓炎谱系疾病:临床与影像学表现
JBR-BTR. 2007 Jul-Aug;90(4):284-7.
6
[Devic's neuro-optic myelitis and pregnancy].
J Fr Ophtalmol. 2007 Sep;30(7):737-43. doi: 10.1016/s0181-5512(07)91363-7.
7
A Comprehensive Management of Devic's Disease: A Pediatric Case Study.设备相关疾病的综合管理:一项儿科病例研究。
Cureus. 2024 Jun 17;16(6):e62512. doi: 10.7759/cureus.62512. eCollection 2024 Jun.
8
[Neuromyelitis optica/Devic's syndrome: new perspectives].[视神经脊髓炎/德维克综合征:新视角]
Rev Med Suisse. 2007 Apr 11;3(106):950-5.
9
Neuromyelitis optica (Devic's syndrome) in two sisters.两姐妹患视神经脊髓炎(德维克综合征)。
Clin Electroencephalogr. 1982 Jan;13(1):36-9. doi: 10.1177/155005948201300104.
10
Devic's neuromyelitis optica and pregnancy: distinction from multiple sclerosis is essential.视神经脊髓炎谱系疾病与妊娠:与多发性硬化症相鉴别至关重要。
Arch Gynecol Obstet. 2009 Sep;280(3):475-7. doi: 10.1007/s00404-008-0918-7. Epub 2009 Jan 17.

引用本文的文献

1
Histological and Top-Down Proteomic Analyses of the Visual Pathway in the Cuprizone Demyelination Model.铜螯合剂诱导脱髓鞘模型中视觉通路的组织学和自上而下蛋白质组学分析
J Mol Neurosci. 2022 Jun;72(6):1374-1401. doi: 10.1007/s12031-022-01997-w. Epub 2022 May 30.
2
Patient-reported outcome measure for neuromyelitis optica: pretesting of preliminary instrument and protocol for further development in accordance with international guidelines.视神经脊髓炎患者报告结局量表:初步工具的预测试及依据国际指南进行进一步开发的方案
BMJ Open. 2016 Sep 30;6(9):e011142. doi: 10.1136/bmjopen-2016-011142.
3
White and Gray Matter Volume Changes and Correlation with Visual Evoked Potential in Patients with Optic Neuritis: A Voxel-Based Morphometry Study.

本文引用的文献

1
Neuromyelitis optica: concepts in evolution.视神经脊髓炎:演进中的概念。
J Neuroimmunol. 2011 Feb;231(1-2):100-4. doi: 10.1016/j.jneuroim.2010.10.012. Epub 2010 Nov 9.
2
EFNS guidelines on diagnosis and management of neuromyelitis optica.EFNS 指南:视神经脊髓炎的诊断与管理。
Eur J Neurol. 2010 Aug;17(8):1019-32. doi: 10.1111/j.1468-1331.2010.03066.x. Epub 2010 Jun 7.
3
Detection of anti-aquaporin-4 antibodies in neuromyelitis optica: current status of the assays.视神经脊髓炎中抗水通道蛋白4抗体的检测:检测方法的现状
视神经炎患者白质和灰质体积变化及其与视觉诱发电位的相关性:基于体素的形态学研究
Med Sci Monit. 2016 Apr 5;22:1115-23. doi: 10.12659/msm.897837.
Int MS J. 2008 Sep;15(3):99-105.
4
Characteristics of Devic's disease (neuromyelitis optica) in Mexico.墨西哥视神经脊髓炎谱系疾病(德维克病)的特征。
J Neurol. 2008 May;255(5):710-5. doi: 10.1007/s00415-008-0781-2. Epub 2008 Feb 19.
5
Revised diagnostic criteria for neuromyelitis optica.视神经脊髓炎修订诊断标准。
Neurology. 2006 May 23;66(10):1485-9. doi: 10.1212/01.wnl.0000216139.44259.74.
6
IgG marker of optic-spinal multiple sclerosis binds to the aquaporin-4 water channel.视神经脊髓型多发性硬化症的IgG标志物与水通道蛋白4水通道结合。
J Exp Med. 2005 Aug 15;202(4):473-7. doi: 10.1084/jem.20050304. Epub 2005 Aug 8.
7
Devic's neuromyelitis optica: clinical features and prognostic factors.视神经脊髓炎谱系疾病:临床特征与预后因素
Neurol Sci. 2004 Nov;25 Suppl 4:S364-7. doi: 10.1007/s10072-004-0342-0.
8
A serum autoantibody marker of neuromyelitis optica: distinction from multiple sclerosis.视神经脊髓炎的一种血清自身抗体标志物:与多发性硬化症的区别。
Lancet. 2004;364(9451):2106-12. doi: 10.1016/S0140-6736(04)17551-X.
9
Clinical characteristics, course and prognosis of relapsing Devic's Neuromyelitis Optica.复发性视神经脊髓炎的临床特征、病程及预后
J Neurol. 2004 Jan;251(1):47-52. doi: 10.1007/s00415-004-0271-0.
10
The clinical course of neuromyelitis optica (Devic's syndrome).视神经脊髓炎(德维克综合征)的临床病程。
Neurology. 1999 Sep 22;53(5):1107-14. doi: 10.1212/wnl.53.5.1107.