[右优势型完全性房室通道合并右心室双出口、共同房室瓣反流的改良Fontan手术1例]

[A case of modified Fontan operation for complete atrioventricular canal of right dominance with double-outlet right ventricle, common atrioventricular valve regurgitation].

作者信息

Eishi K, Hata T, Taniguchi G, Shinoka S, Namba H, Sone Y, Takata S, Kuinose M, Ueda M, Mori K

机构信息

Department of Cardiovascular Surgery, Cardiovascular Center Sakakibara Hospital.

出版信息

Kyobu Geka. 1990 Feb;43(2):147-50.

PMID:2308248

Abstract

A 6-year-old boy was diagnosed to have complete atrioventricular canal (CAVC) with double-outlet right ventricle (DORV), common atrium and common atrioventricular valve regurgitation. The atrioventricular junction predominantly connected to the right ventricle (right dominance) and the left ventricle was hypoplastic (LVEDV = 64% of normal). The combination of DORV with right dominant CAVC makes more difficult to make intra-ventricular rerouting. A modified Fontan procedure, atrial partition and DeVega's annuloplasty were successfully performed. It is concluded that Fontan procedure might be preferable rather than intra-ventricular rerouting in this case.

摘要

一名6岁男孩被诊断为完全性房室通道（CAVC）合并右心室双出口（DORV）、共同心房和共同房室瓣反流。房室连接主要连接到右心室（右优势型），左心室发育不良（左心室舒张末期容积 = 正常的64%）。DORV合并右优势型CAVC使得心室内部改道更加困难。成功实施了改良Fontan手术、心房分隔和德维加瓣环成形术。得出的结论是，在这种情况下，Fontan手术可能比心室内部改道更可取。