Dept of Pathology, Department of Medicine, Duke University Medical Center,Durham, NC 27710, USA.
Am J Clin Pathol. 2012 Dec;138(6):855-66. doi: 10.1309/AJCPOP7APGDT9JIU.
We describe 41 cases of myeloid neoplasms (MNs) secondary to plasma cell myeloma (PCM). The types of MN included myelodysplastic syndrome (MDS) in 34 (82.9%), acute myeloid leukemia (AML) in 4 (9.8%), and myeloproliferative neoplasm (MPN) or MDS/MPN in 3 (7.3%) cases. The latency from treatment to diagnosis of MN ranged from 9 to 384 months, with a median of 60 months. Of 37 cases with cytogenetic studies, complex abnormalities were detected in 22 (59.5%), -5(q)/-7(q) in 4 (10.8%), other abnormalities in 8 (21.6%), and normal karyotype in 3 (8.1%) cases. Complex abnormalities and -5(q)/-7(q) correlated directly with multiple chemotherapeutic regimens, particularly with combined melphalan/cyclophosphamide. Moreover, the features of cytogenetic abnormalities in our series were significantly different from those with concomitant PCM/MN who had significantly lower complex abnormalities. The latency, skewed proportion of MDS, and bias toward complex cytogenetic abnormalities/unbalanced aberrations of chromosomes 5/7 suggested an alkylating mutagenic effect on pathogenesis of secondary MN. Kaplan-Meier survival analysis demonstrated a median survival of 19 months, which was better than that for therapy-related (t)-MDS/AML. In contrast to t-MDS, the survival in our patients appeared to depend on subtypes of MDS as seen in de novo diseases.
我们描述了 41 例继发于浆细胞骨髓瘤(PCM)的骨髓增生异常肿瘤(MNs)。MN 的类型包括 34 例(82.9%)骨髓增生异常综合征(MDS)、4 例(9.8%)急性髓系白血病(AML)和 3 例(7.3%)骨髓增生性肿瘤(MPN)或 MDS/MPN。从治疗到 MN 诊断的潜伏期为 9 至 384 个月,中位数为 60 个月。在 37 例有细胞遗传学研究的病例中,22 例(59.5%)检测到复杂异常,4 例(10.8%)-5(q)/-7(q),8 例(21.6%)有其他异常,3 例(8.1%)核型正常。复杂异常和-5(q)/-7(q)与多种化疗方案直接相关,特别是与联合美法仑/环磷酰胺。此外,我们的系列中细胞遗传学异常的特征与同时伴有 PCM/MN 的患者明显不同,后者复杂异常明显较低。潜伏期、MDS 偏斜比例以及对复杂细胞遗传学异常/染色体 5/7 不平衡畸变的偏好提示烷基化诱变剂对继发性 MN 的发病机制有影响。Kaplan-Meier 生存分析显示中位生存时间为 19 个月,优于治疗相关(t)-MDS/AML。与 t-MDS 不同,我们患者的生存似乎取决于初发疾病中 MDS 的亚型。