Georgia Health Sciences University, Department of General Surgery, Augusta, GA 30912, USA.
J Pediatr Surg. 2012 Dec;47(12):e55-9. doi: 10.1016/j.jpedsurg.2012.09.052.
Bizarre parosteal osteochondromatous proliferation (BPOP), or Nora's lesion, was first described by Nora et al. in 1983 as a rare, tumor-like lesion involving the bones of the hands and feet. Popliteal artery pseudoaneursyms in the pediatric population are also unusual. Here, we present a case of a young male with a popliteal artery pseudoaneurysm and distal femur lesion originally thought to be an osteochondroma. A 10-year old, Caucasian male was referred to our facility following an MRI concerning for a popliteal artery pseudoaneurysm. On physical exam, there was a palpable 5 × 5-cm pulsatile mass in the upper popliteal fossa with a normal pulse exam bilaterally. A computed tomographic angiogram demonstrated a 4.5-cm by 1.8-cm by 3.6-cm pseudoaneurysm adherent to a 3.5-cm thick, exostotic lesion of the posterior right femur. He was taken to the operating room for repair of the popliteal pseudoaneurysm and resection of his bone lesion. The final pathology was consistent with a popliteal pseudoaneurysm, osteochondroma, and bizarre parosteal osteochondromatous proliferation (BPOP), otherwise known as Nora's lesion. The location of the lesion and the age of our patient were both atypical for BPOP and to our knowledge, this represents the first report of a resulting popliteal artery pseudoaneurysm.
奇异骨旁骨软骨瘤性增殖(BPOP),或 Nora 病变,于 1983 年由 Nora 等人首次描述为一种罕见的、类似肿瘤的病变,涉及手部和足部骨骼。儿童人群中的腘动脉假性动脉瘤也不常见。在这里,我们报告了一例年轻男性的病例,他患有腘动脉假性动脉瘤和股骨远端病变,最初被认为是骨软骨瘤。一名 10 岁的白人男性因 MRI 检查发现疑似腘动脉假性动脉瘤而被转诊至我们的医疗机构。体格检查时,在上腘窝处可触及一个 5×5cm 的搏动性肿块,双侧脉搏检查正常。计算机断层血管造影显示一个 4.5×1.8×3.6cm 的假性动脉瘤附着在右股骨后侧 3.5cm 厚的外生性病变上。他被送往手术室修复腘动脉假性动脉瘤并切除骨病变。最终的病理结果与腘动脉假性动脉瘤、骨软骨瘤和奇异骨旁骨软骨瘤性增殖(BPOP)一致,也称为 Nora 病变。该病变的位置和患者的年龄对于 BPOP 来说都不典型,据我们所知,这是首例报告的导致腘动脉假性动脉瘤的病例。