Puronen Camille E, Josephson Neil C, Broudy Virginia C
Department of Medicine, Harborview Medical Center, Seattle, WA 98104, USA.
Blood Coagul Fibrinolysis. 2013 Jun;24(4):430-2. doi: 10.1097/MBC.0b013e32835bfdde.
Acquired von Willebrand syndrome (AVWS) is a rare bleeding disorder that typically presents as mucocutaneous bleeding in individuals with no personal or family history of bleeding disorder. Here we present a case in which a patient presented with profound epistaxis and was found to have AVWS in the setting of monoclonal gammopathy of undetermined significance (MGUS).
获得性血管性血友病综合征(AVWS)是一种罕见的出血性疾病,通常表现为无个人或家族出血性疾病史的个体出现黏膜皮肤出血。在此,我们报告一例患者,该患者出现严重鼻出血,在意义未明的单克隆丙种球蛋白病(MGUS)背景下被发现患有AVWS。