Arenander H, Rödl W
Röntgenabteilung Zentrum Innere Medizin der Universität Erlangen-Nürnberg.
Radiologe. 1990 Jan;30(1):29-31.
We report the rare case of a 27-year-old man with decompensated cirrhosis of the liver caused by a deficiency of alpha-1-antitrypsin. The patient was scheduled for liver transplantation. Diagnostic procedures prior to surgery revealed an unusual hepatofugal collateral channel with a marked mesenterico-, lieno-, and renocaval shunt. Since the liver cirrhosis had already been manifest during early infancy, this shunt had formed spontaneously without developing esophagogastric varices.
我们报告了一例罕见病例，一名27岁男性因α-1-抗胰蛋白酶缺乏导致失代偿性肝硬化。该患者计划接受肝移植。术前诊断检查发现一条异常的肝外分流支，伴有明显的肠系膜、脾和肾腔静脉分流。由于肝硬化在婴儿早期就已出现，这条分流支是自发形成的，未出现食管胃静脉曲张。
