肠系膜脂肪营养不良——一种罕见的腹内肿物。
Mesenteric lipodystrophy - An unusual intraabdominal mass.
作者信息
McDermott R L, Hutchinson B, Ryan C, Conneely J B, Latif A, Maguire D, Sheahan K
机构信息
Department of General and Hepatopbiliary Surgery, St. Vincent's University Hospital, Elm Park, Dublin 4, Ireland.
出版信息
Int J Surg Case Rep. 2013;4(2):232-4. doi: 10.1016/j.ijscr.2012.11.024. Epub 2012 Dec 8.
INTRODUCTION
We report the case of a 21 year old female with underlying facial lipodystrophy who presented with left lower abdominal pain, weight gain and altered bowel habit.
PRESENTATION OF CASE
Subsequent investigation showed a large (21cm×18cm×8cm) intraabdominal mass. At laparotomy, it was completely excised and was seen to arise from the transverse mesocolon and following histology revealed it to be mesenteric lipodystrophy.
DISCUSSION
Mesenteric lipodystrophy is a rare clinical entity, and part of a spectrum of disorders of sclerosing mesenteritis. This is the first reported case in a patient with pre-existing facial lipodystrophy.
CONCLUSION
Herein we describe a case of mesenteric lipodystrophy, discuss its management and review of the literature.
引言
我们报告一例21岁患有潜在面部脂肪营养不良的女性病例，该患者出现左下腹疼痛、体重增加和排便习惯改变。
病例介绍
后续检查发现一个巨大的（21cm×18cm×8cm）腹腔内肿块。在剖腹手术中，将其完全切除，发现肿块起源于横结肠系膜，组织学检查显示为肠系膜脂肪营养不良。
讨论
肠系膜脂肪营养不良是一种罕见的临床病症，是硬化性肠系膜炎症谱系疾病的一部分。这是首例报道的患有既往面部脂肪营养不良的患者。
结论
在此我们描述一例肠系膜脂肪营养不良病例，讨论其治疗方法并进行文献综述。
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