Department of Neurology, Inselspital, University Hospital Bern, Bern, Switzerland.
Neurology. 2013 Jan 8;80(2):e20. doi: 10.1212/WNL.0b013e31827b90f9.
A 57-year-old man with genetically proven facioscapulohumeral muscular dystrophy (FSHMD 1A) demonstrated Beevor sign (video on the Neurology Web site at www.neurology.org). The upward movement of the umbilicus in a supine patient flexing the neck or sitting up is named after the British neurologist Charles Edward Beevor (1854-1908). He described a "marked elevation of the umbilicus in the act of sitting up" due to a paralyzed infraumbilical part of the rectus abdominis muscle, indicating a lesion of the spinal cord between the segments T10 and T12 or its nerve roots.(1) Beevor sign may also be present, as in our patient, in myopathies affecting the abdominal muscles, particularly in FSHMD, in which predominant involvement of the lower part of the rectus abdominis muscle is typical.(2).
一位 57 岁的男性患有遗传性面肩肱型肌营养不良症(FSHMD1A),表现出 Beevor 征(视频可在 Neurology 网站 www.neurology.org 上观看)。仰卧位患者颈部弯曲或坐起时脐向上移动,此现象以英国神经病学家 Charles Edward Beevor(1854-1908)的名字命名。他描述了一种“坐起时脐明显升高”的现象,这是由于腹直肌下脐部的肌肉瘫痪,提示脊髓 T10 和 T12 节段之间或其神经根出现病变。(1) Beevor 征也可能存在,就像我们的患者一样,在影响腹部肌肉的肌病中,特别是在 FSHMD 中,腹直肌下部的明显受累是典型的。(2)。