Sarimski Klaus, Ebner Sarah, Wördemann Claudia
Pädagogische Hochschule Heidelberg.
Prax Kinderpsychol Kinderpsychiatr. 2012;61(9):677-90. doi: 10.13109/prkk.2012.61.9.677.
Parents of 64 children and youths with Prader-Willi syndrome (PWS) describe their children's behaviour on the "Temperament and Atypical Behavior Scale" (TABS) and the German version of the "Developmental Behavior Checklist" (VFE). In the younger age group, there are no specific behavioural abnormalities which characterize a behavioral phenotype. In the older age group the data reveal elevated levels of abnormal behaviors (communication disturbance, social relations and disruptive behaviors). Parents stress ritualistic behaviors as especially challenging. The results concerning form and age-dependency of abnormal behaviors are discussed in the context of prevention and treatment options.
64名普拉德-威利综合征(PWS)患儿及青少年的家长,在“气质与非典型行为量表”(TABS)以及德文版“发育行为检查表”(VFE)中描述了他们孩子的行为。在低龄组中,不存在可表征行为表型的特定行为异常。在高龄组中,数据显示异常行为(沟通障碍、社会关系及破坏性行为)水平升高。家长强调仪式化行为尤其具有挑战性。在预防和治疗选项的背景下,对异常行为的形式及年龄依赖性结果进行了讨论。