University of British Columbia, Department of Pathology & Laboratory Medicine, G227-2211 Wesbrook Mall, Vancouver, British Columbia, Canada V6T2B5.
J Neurol Sci. 2013 Feb 15;325(1-2):142-7. doi: 10.1016/j.jns.2012.12.023. Epub 2013 Jan 11.
Statins are widely used to treat hyperlipidemia and lower cardiovascular disease risk. While statins are generally well tolerated, some patients experience statin-induced myopathy (SIM). Statin treatment has been associated with mitochondrial dysfunction and mitochondrial DNA (mtDNA) depletion. In this retrospective study, skeletal muscle biopsies from patients diagnosed with SIM were studied. These were compared with biopsies from patients clinically assessed as having statin-unrelated myopathy but whose biopsy showed no or negligible pathology. For each biopsy sample, mtDNA was quantified relative to nuclear DNA (mtDNA content) by qPCR, mtDNA deletions were investigated by long-template PCR followed by gel densitometry, and mtDNA oxidative damage was quantified using a qPCR-based assay. For a subset of matched samples, mtDNA heteroplasmy and mutations were investigated by cloning/sequencing. Skeletal muscle mtDNA content was significantly lower in SIM patients (N=23, mean±SD, 2036±1146) than in comparators (N=24, 3220±1594), p=0.006. There was no difference in mtDNA deletion score or oxidative mtDNA damage between the two groups, and no evidence of increased mtDNA heteroplasmy or somatic mutations was detected. The significant difference in skeletal muscle mtDNA suggests that SIM or statin treatments are associated with depletion of skeletal muscle mtDNA or that patients with an underlying predisposition to SIM have lower mtDNA levels. If statins induce mtDNA depletion, this would likely reflect decreased mitochondria biogenesis and/or increased mitochondria autophagy. Further work is necessary to distinguish between the lower mtDNA as a predisposition to SIM or an effect of SIM or statin treatment.
他汀类药物广泛用于治疗高脂血症和降低心血管疾病风险。虽然他汀类药物通常耐受性良好,但有些患者会出现他汀类药物引起的肌肉病变(SIM)。他汀类药物治疗与线粒体功能障碍和线粒体 DNA(mtDNA)耗竭有关。在这项回顾性研究中,研究了诊断为 SIM 的患者的骨骼肌活检。将这些活检与临床评估为与他汀类药物无关的肌肉病变但活检显示无或可忽略的病理的患者的活检进行比较。对于每个活检样本,通过 qPCR 相对于核 DNA(mtDNA 含量)定量 mtDNA,通过长模板 PCR 后凝胶密度测定法研究 mtDNA 缺失,并使用基于 qPCR 的测定法定量 mtDNA 氧化损伤。对于一组匹配的样本,通过克隆/测序研究 mtDNA 异质性和突变。SIM 患者(N=23,平均值±标准差,2036±1146)的骨骼肌 mtDNA 含量明显低于对照组(N=24,3220±1594),p=0.006。两组之间的 mtDNA 缺失评分或氧化 mtDNA 损伤无差异,并且未检测到增加的 mtDNA 异质性或体细胞突变。骨骼肌 mtDNA 的显著差异表明,SIM 或他汀类药物治疗与骨骼肌 mtDNA 的耗竭有关,或者具有 SIM 潜在易感性的患者的 mtDNA 水平较低。如果他汀类药物诱导 mtDNA 耗竭,这可能反映出线粒体生物发生减少和/或线粒体自噬增加。需要进一步的工作来区分较低的 mtDNA 是 SIM 的易感性还是 SIM 或他汀类药物治疗的影响。