Chen S C, deMello D
Department of Pediatrics, St. Louis University School of Medicine, St. Louis.
Chest. 1990 May;97(5):1255-7. doi: 10.1378/chest.97.5.1255.
Postmortem findings in the lungs of two siblings with nonimmune hydrops and lung hypoplasia are presented. In one, a girl, the hypoplasia was severe, with reduced numbers of airway generations and markedly reduced radial alveolar counts. In the other, a boy, the hypoplasia of both airway and alveolar development was mild. The reason for the difference in the growth of the lungs in these two children is unknown. The additional finding of Noonan's syndrome in the male sibling with mild hypoplasia and in the father is of interest.
本文介绍了两名患有非免疫性水肿和肺发育不全的兄弟姐妹肺部的尸检结果。其中一名女孩,肺发育不全严重,气道分支数量减少,肺泡计数显著降低。另一名男孩,气道和肺泡发育的发育不全程度较轻。这两名儿童肺部生长差异的原因尚不清楚。在轻度发育不全的男性兄弟姐妹及其父亲中发现努南综合征这一额外发现很有意思。