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颅底动脉瘤样骨囊肿表现为颈静脉孔综合征并多骨受累。

Skull base aneurysmal bone cyst presented with foramen jugular syndrome and multi-osseous involvement.

作者信息

Aghaghazvini Leila, Sedighi Nahid, Karami Parisa, Yeganeh Omid

机构信息

Department of Radiology, Shariati Hospital, Tehran University of Medical Sciences, Tehran, Iran ; Advanced Diagnostic and Interventional Radiology Research Center (ADIR), Tehran, Iran.

出版信息

Iran J Radiol. 2012 Sep;9(3):157-60. doi: 10.5812/iranjradiol.7952. Epub 2012 Sep 17.

Abstract

Aneurysmal bone cyst (ABC) is an expansile bone lesion that usually involves the long bones. Skull base involvement is rare. Hereby, we describe a 17-year-old man with hoarseness, facial asymmetry, left sided sensorineural hearing loss and left jugular foramen syndrome. CT scan and MRI showed a skull base mass that was confirmed as ABC in histopathology. The case was unusual and interesting due to the clinical presentation of jugular foramen syndrome and radiological findings such as severe enhancement and multiosseous involvement.

摘要

动脉瘤样骨囊肿(ABC)是一种通常累及长骨的膨胀性骨病变。累及颅底的情况罕见。在此,我们描述一名17岁男性,有声音嘶哑、面部不对称、左侧感音神经性听力损失及左侧颈静脉孔综合征。CT扫描和MRI显示颅底有一肿块,组织病理学证实为ABC。该病例因颈静脉孔综合征的临床表现以及如重度强化和多骨受累等影像学表现而不同寻常且有趣。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/095c/3522374/acc2ff49dcd2/iranjradiol-09-157-g001.jpg

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