Hunold P
Klinik für Radiologie und Nuklearmedizin, Universitätsklinikum Schleswig-Holstein, Campus Lübeck, Deutschland.
Radiologe. 2013 Jan;53(1):38-44. doi: 10.1007/s00117-012-2383-3.
Arrhythmogenic right ventricular dysplasia/cardiomyopathy is a congenital disease that may present with sudden cardiac death as the first manifestation. Standards for the difficult clinical diagnosis are the so-called modified Task Force criteria that incorporate imaging-based, electrocardiographic and anamnestic information. Cardiac magnetic resonance imaging (MRI) is the standard technique for imaging of the right ventricle and can compliment the recent ARVD/C diagnosis criteria by providing exact information on right ventricular size and function. It is the most reliable modality available for the detection of right ventricular aneurysms and the quantification of ventricular size. Furthermore, MRI is able to identify areas of fatty or fibrous replacement within the right ventricular myocardium in a non-invasive way. However, a suspicion of ARVD/C cannot be confirmed or excluded based on MRI findings alone. In clinical routine cardiac MRI is an enormously important component in the ARVD/C diagnostic toolbox; however, MRI can only act as one part of the diagnostic puzzle and should exclusively be performed by experienced centers using specifically tailored protocols.
致心律失常性右室发育不良/心肌病是一种先天性疾病，可能以心脏性猝死作为首发表现。临床诊断困难的标准是所谓的改良工作组标准，该标准纳入了基于影像学、心电图和既往史信息。心脏磁共振成像（MRI）是右心室成像的标准技术，通过提供有关右心室大小和功能的确切信息，可以补充最新的致心律失常性右室发育不良/心肌病（ARVD/C）诊断标准。它是检测右心室动脉瘤和量化心室大小最可靠的方法。此外，MRI能够以非侵入性方式识别右心室心肌内的脂肪或纤维替代区域。然而，仅凭MRI检查结果不能确诊或排除ARVD/C。在临床实践中，心脏MRI是ARVD/C诊断工具箱中极为重要的组成部分；然而，MRI只能作为诊断难题的一部分，并且应该仅由经验丰富的中心使用专门定制的方案来进行检查。
