Department of Cardiology, National Heart Centre, Singapore.
Singapore Med J. 2013 Jan;54(1):e1-4.
Patients with long QT syndrome can sometimes present with a ventricular fibrillation (VF) storm. Catheter ablation of culprit premature ventricular complexes responsible for the triggering of the VF episodes may be required in rare cases of electrical storm that do not respond to conventional measures, and this can be life-saving. We describe a case of emergency catheter ablation in a young woman with a normal corrected QT interval, who presented with malignant VF storm for the first time. We also discuss the diagnostic and management challenges involved, as well as the value of genetic testing in refining the diagnosis.
患有长 QT 综合征的患者有时可能会出现心室颤动 (VF) 风暴。在某些情况下，电风暴对常规治疗无效，可能需要对导致 VF 发作的罪魁祸首室性早搏进行导管消融，这可能是救命的。我们描述了一位年轻女性的紧急导管消融病例，该女性在正常校正 QT 间期时首次出现恶性 VF 风暴。我们还讨论了所涉及的诊断和管理挑战，以及基因检测在细化诊断方面的价值。
