Vij Mukul, Jaiswal Sushila, Agrawal Vinita, Jaiswal Awadesh, Behari Sanjay
Christian Medical College, Department of Pathology, Vellore, India.
Turk Neurosurg. 2013;23(1):113-6. doi: 10.5137/1019-5149.JTN.4255-11.1.
Nerve sheath myxoma (neurothekeoma) are rare benign nerve sheath tumors, usually arising in the skin of the head and neck region and upper extremities in young females. To the best of author's knowledge only two cases of intracranial neurothekeoma have been published in the English literature. These tumors were located in the parasellar area and in middle cranial fossa. This is the first case report of cerebellopontine angle neurothekeoma and third case report of intracranial neurothekeoma. This patient, a 45-year-old female, presented to us with complaints of right side progressive hearing loss for 12 months and swaying during walking for 8 months. Histologically the tumor had lobular appearance with spindle or stellate cells embedded in abundant myxoid background. The tumor cells were diffusely positive for S100. The patient was symptom free at eight month follow up.
神经鞘黏液瘤（神经鞘瘤）是一种罕见的良性神经鞘肿瘤，通常发生于年轻女性头颈部和上肢的皮肤。据作者所知，英文文献中仅发表过两例颅内神经鞘瘤的病例。这些肿瘤位于鞍旁区域和中颅窝。这是首例关于桥小脑角神经鞘瘤的病例报告，也是颅内神经鞘瘤的第三例病例报告。该患者为一名45岁女性，因右侧进行性听力下降12个月及行走时摇晃8个月前来就诊。组织学上，肿瘤呈小叶状外观，梭形或星状细胞嵌入丰富的黏液样背景中。肿瘤细胞S100弥漫阳性。患者在随访8个月时无症状。
