Kim Byung-Ho, Park Yon Woong, Hong Seung-Pyo, Son Ja-Yung, Lee Young-Soo, Lee Jin-Bae, Ryu Jae-Kean, Choi Ji-Yong, Kim Kee-Sik, Chang Sung-Guk
Division of Cardiology, Department of Internal Medicine, Daegu Catholic University Medical Center, Daegu, Korea.
J Cardiovasc Ultrasound. 2012 Dec;20(4):197-200. doi: 10.4250/jcu.2012.20.4.197. Epub 2012 Dec 31.
Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is a rare congenital anomaly associated with very high mortality during infancy. We report a 35-year-old female patient with ALCAPA initially visualized by echocardiography. She visited outpatient department presenting with intermittent chest discomfort for 3 weeks. Transthoracic echocardiography showed left coronary artery arising from main pulmonary artery and abundant septal color flow Doppler signals. Transesophageal echocardiography clearly revealed markedly dilated and tortuous right coronary artery showing windsock appearance. Multidetector computed tomography and coronary angiography enabled visualization of anomalous left coronary artery originating from left side of main pulmonary trunk. After treadmill exercise test which showed ST-segment depression presenting inducible myocardial ischemia, patient underwent direct re-implantation of the anomalous coronary artery into the aorta without any complication.
左冠状动脉起源于肺动脉(ALCAPA)是一种罕见的先天性异常,与婴儿期极高的死亡率相关。我们报告了一名35岁的女性ALCAPA患者,最初通过超声心动图发现。她因间歇性胸部不适3周前来门诊就诊。经胸超声心动图显示左冠状动脉起源于主肺动脉,并有丰富的室间隔彩色血流多普勒信号。经食管超声心动图清晰地显示右冠状动脉明显扩张、迂曲,呈风袋样外观。多排螺旋计算机断层扫描和冠状动脉造影能够显示起源于主肺动脉干左侧的异常左冠状动脉。平板运动试验显示ST段压低,提示诱发性心肌缺血,患者随后接受了异常冠状动脉直接重新植入主动脉的手术,无任何并发症。