Tanaka Yusuke, Koyama Shinsuke, Kobayashi Masaki, Kubota Satoshi, Nakamura Ryo, Isobe Masanori, Shiki Yasuhiko
Department of Obstetrics and Gynecology, Osaka Rosai Hospital, Osaka, Japan.
Asian J Endosc Surg. 2013 Feb;6(1):55-7. doi: 10.1111/j.1758-5910.2012.00159.x.
Müllerian duct anomalies are known to cause infertility and reproductive problems. The true incidence of such abnormalities is not well defined. The most widely accepted method of classification for a Müllerian duct anomaly is the American Society of Reproductive Medicine classification (1988). However, there are some rare anomalies inconsistent with the current classification. Herein, we report a rare case of Müllerian duct anomaly, unilateral ovarian and tubal absence with an arcuate uterus. The failure of the Müllerian ducts to canalize can also lead to the development of a unicornuate uterus and adnexal agenesis. An arcuate uterus indicates incomplete septal absorption after normal fusion of the Müllerian ducts. Therefore, its coexistence with adnexal absence and an arcuate uterus is considered to be extremely unlikely.
苗勒管异常已知会导致不孕和生殖问题。此类异常的确切发病率尚不明确。目前被广泛接受的苗勒管异常分类方法是美国生殖医学学会分类法（1988年）。然而，存在一些与当前分类不一致的罕见异常情况。在此，我们报告一例罕见的苗勒管异常病例，即单侧卵巢和输卵管缺如合并弓形子宫。苗勒管未能形成管道也可导致单角子宫和附件发育不全。弓形子宫表明苗勒管正常融合后中隔吸收不完全。因此，其与附件缺如同时存在被认为极不可能。
