Nagoya Akihiro, Kanzaki Ryu, Nakagiri Tomoyuki, Inoue Masayoshi, Susaki Yoshiyuki, Inoue Shinya, Okumura Meinoshin
Department of General Thoracic Surgery, Osaka University Grad uate School of Medicine, Osaka, Japan.
Ann Thorac Cardiovasc Surg. 2014;20 Suppl:531-4. doi: 10.5761/atcs.cr.12.02027. Epub 2013 Jan 31.
Ectopic cervical thymoma (ECT) is a rare tumor that is frequently misdiagnosed as a thyroid tumor or other malignancy. A 34-year-old male with a right palpable neck mass had been mistakenly diagnosed with T-cell lymphoblastic lymphoma even after an open biopsy. The atypical clinical course, including hypogammaglobulinemia, led us to the correct diagnosis; ECT accompanied by Good's syndrome (GS). After the intravenous infusion of gammaglobulin, tumor resection and a subsequent video-assisted thoracoscopic extended thymectomy were performed. The final diagnosis was type AB thymoma, Masaoka stage I. This report is, to the best of our knowledge, the first description of this extremely rare combination.
异位性颈部胸腺瘤（ECT）是一种罕见肿瘤，常被误诊为甲状腺肿瘤或其他恶性肿瘤。一名34岁男性，右侧颈部可触及肿块，即使在开放性活检后仍被误诊为T细胞淋巴母细胞淋巴瘤。包括低丙种球蛋白血症在内的非典型临床病程使我们做出了正确诊断：ECT伴发古德综合征（GS）。静脉输注丙种球蛋白后，进行了肿瘤切除及随后的电视辅助胸腔镜扩大胸腺切除术。最终诊断为AB型胸腺瘤，马萨oka分期I期。据我们所知，本报告是对这种极其罕见组合的首次描述。
