Manieri S, Adurno G, Iorio F, Tomasco B, Vairo U
Unit of Pediatrics, San Carlo Hospital, Potenza, Italy.
Minerva Pediatr. 2013 Feb;65(1):93-6.
Congenital left ventricular diverticulum is a rare condition. When found, it is usually accompanied by other intracardiac malformations, so that again further examination is indicated. Furthermore, it is usually associated with thoracoabdominal wall defect, as seen in the spectrum of Cantrell's pentalogy, a congenital anomaly consisting of a lower sternal defect, diastasis recti, pericardial defect, anterior diaphragmatic hernia and cardiac malformation. This paper reports a case of Cantrell's Syndrome with left ventricular diverticulum. Successful total correction of ventricular diverticulum, ventricular defects and diastasi recti, was performed at two years of age. The clinical features, ambryology and surgical management of these defects are discussed.
先天性左心室憩室是一种罕见的病症。一经发现,通常伴有其他心脏内畸形,因此需要进一步检查。此外,它通常与胸腹壁缺损有关,如在坎特雷尔五联症谱系中所见,这是一种先天性异常,由胸骨下部缺损、腹直肌分离、心包缺损、前膈疝和心脏畸形组成。本文报告一例伴有左心室憩室的坎特雷尔综合征病例。在患儿两岁时成功地对心室憩室、心室缺损和腹直肌分离进行了全面矫正。文中讨论了这些缺损的临床特征、胚胎学和外科治疗方法。