Chen L J, Wu J M, Yang Y J, Wang J N, Lin C S
Department of Pediatrics, National Cheng Kung University Hospital, Tainan,ROC.
J Formos Med Assoc. 1997 Apr;96(4):288-90.
Cantrell's syndrome is a rare combination of congenital midline thoracoabdominal defects and congenital heart disease. surgical repair can correct many of the anomalies. We report a neonate who presented with a short sternum, defective upper abdominal muscle, ectopic umbilicus, anterior diaphragmatic defect, ventricular septal defect and an intra-abdominal left ventricular diverticulum. Initially, the infant was treated with digoxin and diuretics for 5 months. Due to poor control of heart failure, one-stage surgical correction was performed with patch repair of the ventricular septal defect, ligation of left ventricular diverticulum and closure of the defects of the diaphragm and upper abdominal wall.
坎特雷尔综合征是一种先天性胸腹部中线缺陷与先天性心脏病的罕见组合。手术修复可纠正许多此类异常情况。我们报告了一名新生儿,其表现为胸骨短小、上腹部肌肉缺损、脐异位、前膈缺损、室间隔缺损和腹腔内左心室憩室。最初,该婴儿接受了5个月的地高辛和利尿剂治疗。由于心力衰竭控制不佳,遂进行了一期手术矫正,包括室间隔缺损补片修补、左心室憩室结扎以及膈肌和上腹壁缺损修补。