First Department of Internal Medicine, University of Toyama, 2630 Sugitani, Toyama, Toyama 930-0194, Japan.
Age Ageing. 2013 May;42(3):409-10. doi: 10.1093/ageing/aft034. Epub 2013 Mar 18.
Cytophagic histiocytic panniculitis is a chronic histiocytic disease of the subcutaneous adipose tissue characterised by lobular panniculitis with histiocytes containing blood cell fragments. It is also associated with marked systemic features such as fever, pancytopenia, hepatosplenomegaly, liver abnormalities and coagulopathy. We report a case of cytophagic histiocytic panniculitis in a 74-year-old man successfully treated using combination therapy with prednisolone and cyclosporine A.
噬血细胞性组织细胞脂膜炎是一种慢性组织细胞疾病，其特征为具有含血细胞碎片的组织细胞的小叶性脂膜炎。它还与明显的全身特征相关，如发热、全血细胞减少、肝脾肿大、肝异常和凝血功能障碍。我们报告了一例 74 岁男性噬血细胞性组织细胞脂膜炎病例，成功地使用泼尼松龙和环孢素 A 的联合治疗进行治疗。
