Bouchikhi Ahmed Amine, Mellas Soufiane, Tazi Mohammed Fadl, Lahlaidi Karim, Kharbach Youssef, Benhayoune Khadija, Kanab Rajae, Elammari Jalal Eddine, Khallouk Abdelhak, El Fassi Mohammed Jamal, Farih My Hassan
Service d'Urologie, Centre Hospitalier Universitaire de Fès, Fès, Maroc.
J Med Case Rep. 2013 Apr 5;7:93. doi: 10.1186/1752-1947-7-93.
An embryonic paratesticular rhabdomyosarcoma is a very rare mesenchymal tumor. It is an intrascrotal tumor that is localized in paratesticular structures such as the epididymis or spermatic cord. Rhabdomyosarcoma is most often observed in children and adolescents, presenting as a painless scrotal mass.
Our patient was an 18-year-old Moroccan man who presented with a painless left scrotal mass that had evolved over four months. An inguinal orchiectomy was performed. A histological examination of the excised tissue revealed an embryonic rhabdomyosarcoma.Our patient had three sessions of chemotherapy with vincristine, actinomycin C and cyclophosphamide. Each chemotherapy session was conducted over five days, with a cycle of 21 days. Our patient was assessed two months after the last chemotherapy session and demonstrated good clinical improvement.
Paratesticular rhabdomyosarcoma is a rare aggressive tumor manifesting in children and very young adults. Localized forms have a good prognosis whereas metastatic tumors show very poor results. A well-defined treatment based on surgery and chemotherapy yields good results.
胚胎型睾丸旁横纹肌肉瘤是一种非常罕见的间叶组织肿瘤。它是一种位于阴囊内的肿瘤,局限于睾丸旁结构,如附睾或精索。横纹肌肉瘤最常发生于儿童和青少年,表现为无痛性阴囊肿块。
我们的患者是一名18岁的摩洛哥男性,他出现无痛性左侧阴囊肿块,病程已达四个月。进行了腹股沟睾丸切除术。对切除组织的组织学检查显示为胚胎型横纹肌肉瘤。我们的患者接受了三个疗程的化疗,使用长春新碱、放线菌素C和环磷酰胺。每个化疗疗程持续五天,周期为21天。在最后一个化疗疗程两个月后对患者进行评估,结果显示临床状况有明显改善。
睾丸旁横纹肌肉瘤是一种罕见的侵袭性肿瘤,多见于儿童和非常年轻的成年人。局限性肿瘤预后良好,而转移性肿瘤预后很差。基于手术和化疗的明确治疗方案可取得良好效果。