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睾丸旁横纹肌肉瘤:叙利亚的一例罕见病例报告。

Paratesticular rhabdomyosarcoma: a rare case report from Syria.

作者信息

Sabbagh Aziz, Hamza Amr, Sukkari Mohamad Walid, Fattal Abdualh, Chammout Anwar, Ayoub Kusay, Al-Hadid Ibrahim

机构信息

Department of Urology.

Department of Internal Medicine.

出版信息

Ann Med Surg (Lond). 2023 Apr 3;85(5):1928-1931. doi: 10.1097/MS9.0000000000000461. eCollection 2023 May.

Abstract

UNLABELLED

Paratesticular rhabdomyosarcoma (RMS) is a rare aggressive tumor manifesting in children and young adults. This tumor derives from mesenchymal elements of the Tunica vaginalis, epididymis, and spermatic cord. It is a very metastatic lesion that can spread by lymphatics to the iliac, para-aortic nodes, lung, and bone.

CASE PRESENTATION

In this paper, the authors report a case of a 6-year-old child who presented to the clinic with a painless mass in the right side of the scrotum. The mass was misdiagnosed and had evolved rapidly over 2 weeks. The mass measured 16×32 mm on ultrasound, and therefore, an orchiectomy was performed. The histological examination of the excised tissue confirmed the diagnosis of paratesticular RMS.

DISCUSSION

Paratesticular RMS mainly presented as a painless mass in the scrotum. It was a very metastatic lesion that required an immediate management. However, a lot of cases of paratesticular RMS misdiagnosed at first time, which worsens the overall prognosis.

CONCLUSION

Eventually, paratesticular RMS should be always taken into consideration when a scrotal mass is suspected. Due to its extremely serious metastatic potential, this condition requires early diagnosis and management. The treatment is currently well codified combining surgery, chemotherapy, and radiotherapy.

摘要

未标注

睾丸旁横纹肌肉瘤(RMS)是一种罕见的侵袭性肿瘤,多见于儿童和青年。该肿瘤起源于鞘膜、附睾和精索的间充质成分。它是一种极易转移的病变,可通过淋巴管扩散至髂淋巴结、腹主动脉旁淋巴结、肺和骨。

病例报告

在本文中,作者报告了一例6岁儿童,因右侧阴囊无痛性肿块就诊。该肿块被误诊,且在2周内迅速发展。超声检查显示肿块大小为16×32毫米,因此进行了睾丸切除术。切除组织的组织学检查确诊为睾丸旁RMS。

讨论

睾丸旁RMS主要表现为阴囊无痛性肿块。它是一种极易转移的病变,需要立即处理。然而,许多睾丸旁RMS病例起初被误诊,这会使总体预后恶化。

结论

最终,当怀疑有阴囊肿块时,应始终考虑睾丸旁RMS。由于其极高的转移潜能,这种情况需要早期诊断和处理。目前,结合手术、化疗和放疗的治疗方法已得到很好的规范。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7338/10205304/39103c818461/ms9-85-1928-g001.jpg

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