Sabbagh Aziz, Hamza Amr, Sukkari Mohamad Walid, Fattal Abdualh, Chammout Anwar, Ayoub Kusay, Al-Hadid Ibrahim
Department of Urology.
Department of Internal Medicine.
Ann Med Surg (Lond). 2023 Apr 3;85(5):1928-1931. doi: 10.1097/MS9.0000000000000461. eCollection 2023 May.
Paratesticular rhabdomyosarcoma (RMS) is a rare aggressive tumor manifesting in children and young adults. This tumor derives from mesenchymal elements of the Tunica vaginalis, epididymis, and spermatic cord. It is a very metastatic lesion that can spread by lymphatics to the iliac, para-aortic nodes, lung, and bone.
In this paper, the authors report a case of a 6-year-old child who presented to the clinic with a painless mass in the right side of the scrotum. The mass was misdiagnosed and had evolved rapidly over 2 weeks. The mass measured 16×32 mm on ultrasound, and therefore, an orchiectomy was performed. The histological examination of the excised tissue confirmed the diagnosis of paratesticular RMS.
Paratesticular RMS mainly presented as a painless mass in the scrotum. It was a very metastatic lesion that required an immediate management. However, a lot of cases of paratesticular RMS misdiagnosed at first time, which worsens the overall prognosis.
Eventually, paratesticular RMS should be always taken into consideration when a scrotal mass is suspected. Due to its extremely serious metastatic potential, this condition requires early diagnosis and management. The treatment is currently well codified combining surgery, chemotherapy, and radiotherapy.
睾丸旁横纹肌肉瘤(RMS)是一种罕见的侵袭性肿瘤,多见于儿童和青年。该肿瘤起源于鞘膜、附睾和精索的间充质成分。它是一种极易转移的病变,可通过淋巴管扩散至髂淋巴结、腹主动脉旁淋巴结、肺和骨。
在本文中,作者报告了一例6岁儿童,因右侧阴囊无痛性肿块就诊。该肿块被误诊,且在2周内迅速发展。超声检查显示肿块大小为16×32毫米,因此进行了睾丸切除术。切除组织的组织学检查确诊为睾丸旁RMS。
睾丸旁RMS主要表现为阴囊无痛性肿块。它是一种极易转移的病变,需要立即处理。然而,许多睾丸旁RMS病例起初被误诊,这会使总体预后恶化。
最终,当怀疑有阴囊肿块时,应始终考虑睾丸旁RMS。由于其极高的转移潜能,这种情况需要早期诊断和处理。目前,结合手术、化疗和放疗的治疗方法已得到很好的规范。