Burakovskiĭ V I, Bukharin V A, Podzolkov V I, Fal'kovskiĭ G E, Ragimov F R
Grud Serdechnososudistaia Khir. 1990(1):4-10.
In the period of 1980 to February 1988, 60 patients aged 1 year 7 months to 23.5 years were operated on for concordant atrioventricular linkage and origin of the aorta and pulmonary artery from the right ventricle. Sixty-two heart specimens were examined to study the defect anatomy. The left ventricular outlet opened up in the subaortic cone (Type A defect) in 47 (78.3%) patients, in the common subaortic and subpulmonary cone (Type B) in 8 (13.4%) patients, in the subpulmonary cone (Type C) in 3 (5%) patients; 2 (3.3%) subjects exhibited nonconcomitant ventricular septal defect (Type D). Thirty-four (56%) patients had pulmonary stenosis. Concomitant heart diseases were found in 78%. Fifteen patients (25%) underwent radical operation after prior palliative interventions. The total fatal cases were 13.7% (out of 58 operated patients, 8 died) in the group of radically operated patients. The fatal outcomes were observed in Type A defect. The analysis showed that defect correction techniques, age, prior palliative interventions, presence or absence of pulmonary stenosis, concurrent heart diseases, and restrictive ventricular septal defect failed to affect the immediate result of surgeries. An inaccurate preoperative diagnosis and lack of surgical experiment were factors increasing the risk for correction from 1980 to 1986. In the 2 years, the death rates decreased from 17.9% (7 dead patients per 39 operated ones) to 5.3% (1 dead patient per 19 radically operated ones).
在1980年至1988年2月期间，对60例年龄在1岁7个月至23.5岁之间的患者进行了手术，这些患者存在房室一致连接以及主动脉和肺动脉均起源于右心室的情况。对62个心脏标本进行了检查以研究缺损解剖结构。47例（78.3%）患者的左心室出口通向主动脉下圆锥（A型缺损），8例（13.4%）患者通向共同的主动脉下和肺动脉下圆锥（B型），3例（5%）患者通向肺动脉下圆锥（C型）；2例（3.3%）患者存在不合并室间隔缺损（D型）。34例（56%）患者有肺动脉狭窄。78%的患者发现合并有其他心脏病。15例（25%）患者在先前的姑息性干预后接受了根治性手术。在接受根治性手术的患者组中，总死亡率为13.7%（58例手术患者中有8例死亡）。A型缺损出现了致命结果。分析表明，缺损矫正技术、年龄、先前的姑息性干预、有无肺动脉狭窄、合并的心脏病以及限制性室间隔缺损均未影响手术的近期结果。1980年至1986年期间，术前诊断不准确和缺乏手术经验是增加矫正风险的因素。在这两年中，死亡率从17.9%（39例手术患者中有7例死亡）降至5.3%（19例根治性手术患者中有1例死亡）。
