Barreiros Hugo Marques, Serrano Pedro Nuno, Parreira José Carlos, Bártolo Elvira
Department of Dermatology, Hospital Garcia de Orta, Almada, Portugal;
J Dermatol Case Rep. 2013 Mar 30;7(1):27-8. doi: 10.3315/jdcr.2013.1133.
Dermatofibrosarcoma protuberans is an uncommon soft tissue neoplasm. In the vast majority of cases it presents as a nodule or a firm tumor that can reach massive dimensions producing the protuberant nodules for which it is named. We report a case of a 34-year-old woman presented at our department with an 8-year history of a small and discretely erythematous supraclavicular atrophic plaque. Skin biopsy lead to the diagnosis of dermatofibrosarcoma protuberans and a wide local excision of the tumor was performed in collaboration with the Plastic Surgery department. In this clinical case we describe an uncommon variant of the disease with minimal clinical manifestation that can cause serious diagnostic difficulties. The small and discrete atrophic plaque of our patient could have been easily ignored with serious clinical and prognostic implications for the patient.
隆突性皮肤纤维肉瘤是一种罕见的软组织肿瘤。在绝大多数病例中，它表现为一个结节或一个坚实的肿瘤，可发展到很大尺寸，产生其得名所由来的突出结节。我们报告一例34岁女性，因锁骨上有一个小的、散在的红斑性萎缩斑块长达8年而就诊于我科。皮肤活检确诊为隆突性皮肤纤维肉瘤，并与整形外科协作对肿瘤进行了广泛局部切除。在本临床病例中，我们描述了该疾病一种罕见的变异型，其临床表现轻微，可导致严重的诊断困难。我们患者的小而散在的萎缩斑块很容易被忽视，对患者有严重的临床和预后影响。
