Sato Mitsuru, Nagaya Kouichi, Hatakeyama Masaharu, Komatsu Tsunehiro
Division of Cardiovascular Surgery, Aomori Prefectural Central Hospital, 2-1-1 Higashi-tsukurimichi, Aomori, Aomori, 030-0913, Japan,
Gen Thorac Cardiovasc Surg. 2014 Feb;62(2):122-4. doi: 10.1007/s11748-013-0249-x. Epub 2013 Apr 23.
A 59-year-old woman with chest discomfort was transferred to our hospital. Echocardiography was suggestive of multiple papillary fibroelastoma (PFE). Tumors on both the left and right coronary cusps were confirmed macroscopically and pathologically and a small tumor was noted microscopically on the non-coronary cusp. Aortic valve replacement was successfully performed. The treatment and recurrence rate of PFE is controversial due to its rarity. Given that multiple tumors were seen in the present case and that possible recurrence has been reported elsewhere, valve replacement may be a better choice for surgical repair than valvoplasty in some cases, such as a single PFE in which plasty may be difficult or multiple PFEs regardless of impaired valve function.
一名59岁胸部不适的女性被转至我院。超声心动图提示多发性乳头肌纤维弹性瘤（PFE）。大体及病理检查证实左、右冠状动脉瓣叶均有肿瘤，非冠状动脉瓣叶显微镜下可见一个小肿瘤。成功实施了主动脉瓣置换术。由于PFE罕见，其治疗方法及复发率存在争议。鉴于本病例中发现多个肿瘤，且其他地方有复发的报道，在某些情况下，瓣膜置换术可能是比瓣膜成形术更好的手术修复选择，比如在单一PFE行成形术可能困难或多个PFE且伴有瓣膜功能受损的情况。
