Wical B S, Tomasi L G
Department of Neurology, University of New Mexico School of Medicine, Albuquerque 87131.
Pediatr Neurol. 1990 May-Jun;6(3):202-5. doi: 10.1016/0887-8994(90)90064-8.
Four patients suffered a distinctive neurologic syndrome after undergoing profound hypothermia and complete circulatory arrest for congenital heart lesion repair. Symptom onset was delayed 24-120 hours postoperatively. The syndrome consists of choreoathetosis and oral-facial dyskinesias, hypotonia, affective changes, and pseudobulbar signs (CHAP). Precise anatomic localization is uncertain. Magnetic resonance imaging of 2 patients did not reveal basal ganglia lesions. Pathogenesis is obscure.
4名患者在接受深度低温和完全循环停滞后出现了一种独特的神经综合征，用于先天性心脏病变修复。症状在术后24 - 120小时出现延迟。该综合征包括舞蹈手足徐动症和口面部运动障碍、肌张力减退、情感变化和假性球麻痹体征（CHAP）。精确的解剖定位尚不确定。2名患者的磁共振成像未显示基底神经节病变。发病机制尚不清楚。
