Marino B, Ballerini L, Soro A
Department of Pediatric Cardiology, Bambino Gesu Hospital Roma, Italy.
Chest. 1990 Jul;98(1):239-41. doi: 10.1378/chest.98.1.239.
We report clinical, angiocardiographic, and anatomic findings of an infant with ventricular inversion (atrioventricular discordance) and truncus arteriosus. The patient was in congestive heart failure and the injections into the left ventricle, right ventricle, and truncus arteriosus allowed a precise diagnosis. The autopsy confirmed this very unusual combination of anomalies and in particular it showed a truncus type 2 completely surrounded by muscular infundibulum and mainly aligned with the right ventricle. Surgical correction of this malformation is a challenge and so far, to our knowledge, has never been reported in the literature.
我们报告了一名患有心室反位（房室不一致）和动脉干的婴儿的临床、心血管造影及解剖学 findings。该患者处于充血性心力衰竭状态，向左心室、右心室和动脉干注射造影剂后得以做出精确诊断。尸检证实了这种非常罕见的异常组合，特别是显示出一个 2 型动脉干完全被肌肉性漏斗部包围且主要与右心室对齐。这种畸形的手术矫正极具挑战性，据我们所知，迄今为止文献中从未有过相关报道。
