Division of Hematology and Hemotherapy, UNIFESP/Escola Paulista de Medicina, São Paulo, SP, CEP: 04037-002, Brazil.
Med Oncol. 2013;30(2):579. doi: 10.1007/s12032-013-0579-7. Epub 2013 May 1.
Acute myeloid leukemia (AML) is a group of clonal diseases, resulting from two classes of mutation. Investigation for additional abnormalities associated with a well-recognized subtype, core-binding factor AML (CBF-AML) can provide further understanding and discrimination to this special group of leukemia. In order to better define genetic alterations in CBF-AML and identify possible cooperating lesions, a single-nucleotide polymorphism-array (SNP-array) analysis was performed, combined to KIT mutation screening, in a set of cases. Validation of SNP-array results was done by array comparative genomic hybridization and FISH. Fifteen cases were analyzed. Three cases had microscopic lesions better delineated by arrays. One case had +22 not identified by arrays. Submicroscopic abnormalities were mostly non-recurrent between samples. Of relevance, four regions were more frequently affected: 4q28, 9p11, 16q22.1, and 16q23. One case had an uncovered unbalanced inv(16) due to submicroscopic deletion of 5´MYH11 and 3´CBFB. Telomeric and large copy number neutral loss of heterozygosity (CNN-LOH) regions (>25 Mb), likely representing uniparental disomy, were detected in four out of fifteen cases. Only three cases had mutation on KIT gene, enhancing the role of abnormalities by SNP-array as presumptive cooperating alterations. Molecular karyotyping can add valuable information to metaphase karyotype analysis, emerging as an important tool to uncover and characterize microscopic, submicroscopic genomic alterations, and CNN-LOH events in the search for cooperating lesions.
急性髓细胞白血病(AML)是一组克隆性疾病,源于两类突变。对与公认的核心结合因子 AML(CBF-AML)亚型相关的其他异常的研究可以为这组特殊的白血病提供进一步的理解和鉴别。为了更好地定义 CBF-AML 中的遗传改变,并识别可能的协同病变,对一组病例进行了单核苷酸多态性微阵列(SNP-array)分析,并结合了 KIT 突变筛选。SNP-array 结果的验证通过 array 比较基因组杂交和 FISH 进行。分析了 15 例。3 例病例的微观病变通过数组更好地描绘。1 例病例的+22 未被数组识别。亚微观异常在样本之间大多是非反复出现的。值得注意的是,四个区域更常受到影响:4q28、9p11、16q22.1 和 16q23。1 例病例由于 5´MYH11 和 3´CBFB 的亚微观缺失,出现未覆盖的不平衡 inv(16)。在 15 例中的 4 例中检测到端粒和大拷贝数中性杂合性丢失(CNN-LOH)区域(>25 Mb),可能代表单亲二体性。仅 3 例病例的 KIT 基因突变,增强了 SNP-array 作为假定协同改变的作用。分子核型分析可以为中期核型分析提供有价值的信息,作为发现和描述微观、亚微观基因组改变以及 CNN-LOH 事件的重要工具,以寻找协同病变。