结节性硬化症合并肝脏及肾脏血管平滑肌脂肪瘤的CT表现
[CT findings of tuberous sclerosis associated with hepatic and renal angiomyolipomas].
作者信息
Li Yue-xing, Xiang Jun-yi, Li Jie, Ding Jian-ping, Lin Shang-qi
机构信息
Department of Radiology, the Affiliated Hospital of Hangzhou Normal University, Hangzhou 310015, China.
出版信息
Zhongguo Yi Xue Ke Xue Yuan Xue Bao. 2013 Apr;35(2):136-9. doi: 10.3881/j.issn.1000-503X.2013.02.002.
OBJECTIVE
To summarize the clinical and computed tomographic(CT) findings of tuberous sclerosis(TS) associated with hepatic and renal angiomyolipomas.
METHOD
We retrospectively analyzed the clinical and CT findings of 7 TS patients with hepatic and renal angiomyolipomas.
RESULTS
Brain CT showed calcified nodules and/or the uncalcified nodule in the lateral ventricle subependymal in 7 patients. Abdominal CT showed bilateral renal angiomyolipomas in 7 cases and hepatic angiomyolipomas in 2 cases. Chest CT showed lymphangioleiomyomatosis in one case.
CONCLUSIONS
TS associated with merger hepatic and/or renal angiomyolipomas have typical CT findings. Liver angiomyolipomas shows certain correlation with bilateral renal angiomyolipomas.
目的
总结结节性硬化症（TS）合并肝脏及肾脏血管平滑肌脂肪瘤的临床及计算机断层扫描（CT）表现。
方法
回顾性分析7例TS合并肝脏及肾脏血管平滑肌脂肪瘤患者的临床及CT表现。
结果
脑部CT显示7例患者侧脑室室管膜下有钙化结节和/或非钙化结节。腹部CT显示7例双侧肾脏血管平滑肌脂肪瘤，2例肝脏血管平滑肌脂肪瘤。胸部CT显示1例淋巴管平滑肌瘤病。
结论
TS合并肝脏和/或肾脏血管平滑肌脂肪瘤有典型的CT表现。肝脏血管平滑肌脂肪瘤与双侧肾脏血管平滑肌脂肪瘤有一定相关性。
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