Department of Vascular Surgery, Freeman's Hospital, Newcastle upon Tyne, United Kingdom.
J Vasc Surg. 2013 Nov;58(5):1385-7. doi: 10.1016/j.jvs.2012.12.081. Epub 2013 Apr 30.
An association has been reported between Wiskott-Aldrich syndrome and necrotizing vasculitis and aneurysmal arterial dilatation. We present here the first endovascular repair of descending thoracic aortic aneurysm in a 35-year-old male patient with the classical Wiskott-Aldrich syndrome phenotype. He had a successful endovascular repair with early discharge from hospital with no postoperative complications. His 1-year follow-up computed tomography scan confirmed appropriate stent position, aneurysm sac resolution with no evidence of endoleak, and no further aneurysm formation.
已报道 Wiskott-Aldrich 综合征与坏死性血管炎和动脉瘤性动脉扩张之间存在关联。我们在此报告首例经典 Wiskott-Aldrich 综合征表型的 35 岁男性患者的降胸主动脉瘤的血管内修复。他的血管内修复成功,术后早期出院,无术后并发症。他的 1 年随访 CT 扫描证实支架位置适当,动脉瘤囊缩小,无内漏证据,且无进一步的动脉瘤形成。